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CC BY 4.0 · European J Pediatr Surg Rep. 2024; 12(01): e11-e15
DOI: 10.1055/a-2206-4825
Case Report

Neonatal Sacrococcygeal Fetiform Teratoma Containing Bowel: A Case Report

Ashley Toms
1   Department of Paediatric surgery, Chris Hani Baragwanath Academic Hospital, Faculty of Health Sciences, University of Witwatersrand, Johannesburg, South Africa
,
Tarlia Rasa Govender
1   Department of Paediatric surgery, Chris Hani Baragwanath Academic Hospital, Faculty of Health Sciences, University of Witwatersrand, Johannesburg, South Africa
,
Giulia Brisighelli 
1   Department of Paediatric surgery, Chris Hani Baragwanath Academic Hospital, Faculty of Health Sciences, University of Witwatersrand, Johannesburg, South Africa
,
Derek Harrison
1   Department of Paediatric surgery, Chris Hani Baragwanath Academic Hospital, Faculty of Health Sciences, University of Witwatersrand, Johannesburg, South Africa
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Abstract

A fetiform sacrococcygeal teratoma (homunculus) is a highly differentiated subgroup of mature cystic teratoma that resembles a malformed fetus. These tumors originate at the base of the coccyx and may vary in their intrapelvic and extrapelvic extent and location. It is important to differentiate this anomaly from fetus-in-fetu which has a higher degree of structural organization. A 5-day-old neonate presented with a type II sacrococcygeal fetiform teratoma. The mass contained both cystic and solid components. Upon surgical excision and coccygectomy, fully formed bowel was found inside the mass, as well as bones and other well-defined structures. The tumor was confirmed to be fully excised and no malignant or immature features were found on histopathological examination. The patient was last seen growing well with an alpha-fetoprotein of 3.5 μg/L, 14 months after resection.

Keywords

sacrococcygeal teratoma - fetiform teratoma - fetus-in-fetu - germ cell tumor

Ethical Approval

This case report received ethical clearance from the human research ethics committee at the University Witwatersrand in Johannesburg.




Publication History

Received: 20 May 2023

Accepted: 21 October 2023

Accepted Manuscript online:
08 November 2023

Article published online:
22 January 2024

© 2024. The Author(s). This is an open access article published by Thieme under the terms of the Creative Commons Attribution License, permitting unrestricted use, distribution, and reproduction so long as the original work is properly cited. (https://creativecommons.org/licenses/by/4.0/)

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